INMEDEA Simulator

Glossary of Diagnoses


 

E76.2 (277.5) Other mucopolysaccharidoses

Superordinate classification: E76 Disorders of glycosaminoglycan metabolism

Inclusive: Beta-glucuronidase deficiency
Mucopolysaccharidosis, types III, IV, VI, VII
Syndrome:
· Maroteaux-Lamy (mild)(severe)
· Morquio(-like)(classic)
· Sanfilippo (type B)(type C)(type D)

 


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